Health Life Media

A Healthier You For A Better Tomorrow

Metabolic Disorders Of Branched Chain Amino Acids

Metabolic Disorders Of Branched Chain Amino Acids Uncategorized

Metabolic Disorders Of Branched Chain Amino Acids

Valine, leucine and isoleucine are branched chain amino acids; an enzyme deficiency can affect their metabolism and lead to an accumulation of organic acids with a severe metabolic acidosis. There are many disorders of branched-chain amino acid metabolism (see table)…