Congenital Periodic Fever Syndromes At A Glance

The innate periodic fever syndromes are inherited diseases which are characterized by repeated fever and other symptoms without another cause.

Most patients develop symptoms during childhood; at less than 10% of them occur only after 18 years. Disorders which have been best described are

The innate periodic fever syndromes are inherited diseases which are characterized by repeated fever and other symptoms without another cause. Most patients develop symptoms during childhood; at less than 10% of them occur only after 18 years. Disorders which have been best described are Familial Mediterranean Fever Hyper-IgD syndrome Tumor necrosis factor (TNF) receptor-associated periodic syndromes include other disorders: the hereditary Kryopyrin-associated periodic syndromes (Kyopyrinopathien) as familial cold autoinflammatory syndrome, Muckle-Wells syndrome and the onset neonatal multisystem inflammatory disease (NOMID) PAPA syndrome (pyogenic arthritis, pyoderma gangrenosum and acne) PFAPA syndrome (periodic fever, aphthous ulcers, stomatitis, pharyngitis and cervical lymphadenitis), may not be hereditary

Health Life Media Team

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