Von Willebrand Syndrome

(Von Willebrand’s disease) The von Willebrand syndrome is a genetic disease in which a lack of von Willebrand factor (vWF) is leading to a platelet dysfunction. Usually a slight bleeding is present. Screening tests show normal platelet counts and occasionally a slightly prolonged PTT. The diagnosis is made by the detection of low vWF antigen levels and an abnormal ristocetin cofactor activity. The treatment consists in a control of bleeding…

September 3, 2018