Variable Protease Sensitive Prionopathie (Vpspr)

The variable protease sensitive Prionopathie (VPSPr) is a rare prion disease (recognized in 2008). VPSPr happens million people at 2-3 / 100. The variable protease sensitive Prionopathie (VPSPr) is a rare prion disease (recognized in 2008). VPSPr happens million people at 2-3 / 100. VPSPr similar to the Gerstmann Scheinker disease (GSS) with respect to the properties of the abnormal prion protein (PrPSc). However, unlike GSS no mutations in the…